Pediatric Radiology

, Volume 42, Issue 12, pp 1510–1513 | Cite as

Congenital high airway obstruction syndrome without tracheoesophageal fistula and with in utero decrease in relative lung size

  • Rieko Furukawa
  • Toshinori Aihara
  • Yuko Tazuke
  • Kosaku Maeda
  • Tomoyuki Kuwata
Case Report


Congenital high airway obstruction syndrome (CHAOS) is diagnosed by characteristic features on US and MRI including fetal upper airway occlusion, lung hyperinflation with an inverted diaphragm, and sometimes massive ascites and hydrops. We describe a case of CHAOS in which improvement in the fetal condition was observed on three sequential fetal MRIs. Such an improvement was thought to represent decrease in intrathoracic pressure caused by a spontaneous perforation such as a tracheoesophageal fistula. However, a fistula was not observed in the present case. Therefore, we suggest that imaging improvements in patients with CHAOS do not always correspond to the presence of a fistula and other factors might contribute to decreasing fetal intrathoracic pressure.


Congenital high airway obstruction syndrome CHAOS EXIT MRI 


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Copyright information

© Springer-Verlag 2012

Authors and Affiliations

  • Rieko Furukawa
    • 1
  • Toshinori Aihara
    • 1
  • Yuko Tazuke
    • 2
  • Kosaku Maeda
    • 2
  • Tomoyuki Kuwata
    • 3
  1. 1.Department of Pediatric Medical ImagingJichi Medical University School of MedicineTochigiJapan
  2. 2.Department of Pediatric SurgeryJichi Medical University School of MedicineTochigiJapan
  3. 3.Department of Obstetrics and GynecologyJichi Medical University School of MedicineTochigiJapan

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