Pediatric Radiology

, Volume 41, Issue 11, pp 1476–1480 | Cite as

Idiopathic infantile arterial calcification in a 12-year-old girl presenting as chronic mesenteric ischemia: imaging findings and angioplasty results

  • Edwin Zhang
  • Richard Owen
  • Garth Bruce
  • Sheldon Wiebe
Case Report


We report an unusual case of chronic mesenteric ischemia presenting in a 12-year-old girl with idiopathic infantile arterial calcinosis (IIAC). This is the first reported case in the literature of chronic mesenteric ischemia in the setting of IIAC. The girl presented with a classical history of postprandial abdominal pain. Imaging demonstrated significant stenoses of the celiac axis, superior mesenteric artery (SMA) and inferior mesenteric artery (IMA). Angioplasty of the celiac axis and SMA was attempted, with successful dilation of the SMA only. At 3-, 6- and 12-month follow-ups, the child’s symptoms had almost resolved. This case report has three important ramifications: chronic mesenteric ischemia is a possible clinical presentation in children with IACC, pre-angioplasty imaging is important in guiding treatment approach, and angioplasty was effective in this case of chronic mesenteric ischemia and offers hope for other similarly affected children.


Idiopathic infantile arterial calcification Chronic mesenteric ischemia Angioplasty CT 


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Copyright information

© Springer-Verlag 2011

Authors and Affiliations

  • Edwin Zhang
    • 1
  • Richard Owen
    • 1
  • Garth Bruce
    • 2
  • Sheldon Wiebe
    • 3
  1. 1.Department of Radiology and Diagnostic ImagingUniversity of AlbertaEdmontonCanada
  2. 2.Department of Pediatrics, Royal University HospitalUniversity of SaskatchewanSaskatoonCanada
  3. 3.Department of Medical Imaging, Royal University HospitalUniversity of SaskatchewanSaskatoonCanada

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