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Pediatric Radiology

, 39:188 | Cite as

Papillary tumor of the pineal region: report of a rapidly progressive tumor with possible multicentric origin

  • Takashi S. Sato
  • Patricia A. Kirby
  • John M. Buatti
  • Toshio MoritaniEmail author
Case Report

Abstract

Papillary tumor of the pineal region (PTPR) is an uncommon tumor recently added to the WHO classification of CNS tumors. We report a case of PTPR in a young boy that was noteworthy for early CSF dissemination and relentless progression. In spite of intensive chemotherapy and comprehensive radiotherapy, the boy died. The neuroimaging appearance is unique with possible multicentric origin of the tumor and intense uptake of 111In-DTPA-pentetreotide.

Keywords

Pineal region tumors Papillary pineal tumor Multicentric Somatostatin receptor 

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Copyright information

© Springer-Verlag 2008

Authors and Affiliations

  • Takashi S. Sato
    • 1
  • Patricia A. Kirby
    • 2
  • John M. Buatti
    • 3
  • Toshio Moritani
    • 4
    Email author
  1. 1.Carver College of MedicineUniversity of IowaIowa CityUSA
  2. 2.Department of PathologyUniversity of IowaIowa CityUSA
  3. 3.Department of Radiation OncologyUniversity of IowaIowa CityUSA
  4. 4.Department of RadiologyUniversity of Iowa Hospitals and ClinicsIowa CityUSA

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