We report the MRI findings in a 3-month-old boy with isolated left ventricular apical hypoplasia. This is a recently described congenital abnormality that consists of an odd, spherically shaped left ventricle due to absence of the ventricular apex. To our knowledge, isolated left ventricular apical hypoplasia has not been reported in a child.
Heart Congenital Cardiomyopathy Isolated left ventricular apical hypoplasia MRI Child
This is a preview of subscription content, log in to check access.
Cine MRBalanced steady-state free precession cine MR in the four chamber view shows the restrictive pattern of the left ventricle with limited contractility. The abnormal origin of the papillary muscles is also displayed. (MPG 161 kb)
Moller JH (1998) Prevalence and incidence of cardiac malformations. In: Moller JH (ed) Surgery of congenital heart disease: Pediatric Cardiac Care Consortium 1984-1995. Futura Publishing, Armonk, NYGoogle Scholar
Didier D, Ratib O (2003) Dynamic cardiovascular MRI. Thieme, New YorkGoogle Scholar
Fernandez-Valls M, Srichai MB, Stillman AE et al (2004) Isolated left ventricular apical hypoplasia: a new congenital anomaly described with cardiac tomography. Heart 90:552–555PubMedCrossRefGoogle Scholar
Bardo D, Frankel DG, Applegate KE et al (2001) Hypoplastic left heart syndrome. Radiographics 21:705–717PubMedGoogle Scholar
Weiford BC, Subbarao VD, Mulhern KM (2004) Noncompaction of the ventricular myocardium. Circulation 109:2965–2971PubMedCrossRefGoogle Scholar
Goo HW, Park IS (2007) Left ventricular noncompaction in an infant: use of non-ECG-gated cardiac CT. Pediatr Radiol 37:217–220PubMedCrossRefGoogle Scholar