Pediatric Radiology

, Volume 37, Issue 7, pp 703–705 | Cite as

MR imaging of isolated left ventricular apical hypoplasia

  • Carlos MarinEmail author
  • Maria Luisa Sanchez
  • Enrique Maroto
  • Silvia Ossaba
  • Yolanda Ruiz
  • Juan I. Zabala
Case Report


We report the MRI findings in a 3-month-old boy with isolated left ventricular apical hypoplasia. This is a recently described congenital abnormality that consists of an odd, spherically shaped left ventricle due to absence of the ventricular apex. To our knowledge, isolated left ventricular apical hypoplasia has not been reported in a child.


Heart Congenital Cardiomyopathy Isolated left ventricular apical hypoplasia MRI Child 

Supplementary material

247_2007_459_MOESM1_ESM.mpg (158 kb)
Cine MR Balanced steady-state free precession cine MR in the four chamber view shows the restrictive pattern of the left ventricle with limited contractility. The abnormal origin of the papillary muscles is also displayed. (MPG 161 kb)


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Copyright information

© Springer-Verlag 2007

Authors and Affiliations

  • Carlos Marin
    • 1
    Email author
  • Maria Luisa Sanchez
    • 1
  • Enrique Maroto
    • 2
  • Silvia Ossaba
    • 1
  • Yolanda Ruiz
    • 1
  • Juan I. Zabala
    • 3
  1. 1.Department of Paediatric RadiologyHospital General Universitario Gregorio MarañónMadridSpain
  2. 2.Department of Paediatric CardiologyHospital General Universitario Gregorio MarañónMadridSpain
  3. 3.Department of Paediatric CardiologyHospital Carlos HayaMalagaSpain

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