Pediatric Radiology

, Volume 37, Issue 1, pp 97–99 | Cite as

Congenital pyriform aperture stenosis

  • Micky OsovskyEmail author
  • Anat Aizer-Danon
  • Gadi Horev
  • Lea Sirota
Case Report


Nasal airway obstruction is a potentially life-threatening condition in the newborn. Neonates are obligatory nasal breathers. The pyriform aperture is the narrowest, most anterior bony portion of the nasal airway, and a decrease in its cross-sectional area will significantly increase nasal airway resistance. Congenital nasal pyriform aperture stenosis (CNPAS) is a rare, unusual form of nasal obstruction. It should be considered in the differential diagnosis of any neonate or infant with signs and symptoms of upper airway compromise. It is important to differentiate this level of obstruction from the more common posterior choanal stenosis or atresia. CNPAS presents with symptoms of nasal airway obstruction, which are often characterized by episodic apnea and cyclical cyanosis.


Congenital nasal pyriform aperture stenosis Neonates 


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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Micky Osovsky
    • 1
    • 3
    Email author
  • Anat Aizer-Danon
    • 2
  • Gadi Horev
    • 2
  • Lea Sirota
    • 1
  1. 1.Department of NeonatologySchneider Pediatric HospitalPetach TikvahIsrael
  2. 2.Department of Pediatric RadiologySchneider Pediatric HospitalPetach TikvahIsrael
  3. 3.Department of Neonatology, Schneider Children’s Medical Center of Israel, Beilinson CampusRabin Medical CenterPetah TikvahIsrael

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