Pediatric Radiology

, Volume 36, Issue 6, pp 566–568 | Cite as

Congenital absence of the portal vein in a child with Turner syndrome

  • Jacob A. Noe
  • Heather C. Pittman
  • Edward M. Burton
Case Report

Abstract

Congenital absence of the portal vein (CAPV) is a rare malformation associated with hepatic encephalopathy and liver function abnormalities. We report a case of a 2-year-old with Turner syndrome, CAPV, and congenital heart malformations.

Keywords

Portal vein absence Turner syndrome Hepatic malformation 

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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Jacob A. Noe
    • 1
  • Heather C. Pittman
    • 2
  • Edward M. Burton
    • 1
  1. 1.Department of Radiology, University of Tennessee College of Medicine–Chattanooga BranchErlanger Health SystemChattanoogaUSA
  2. 2.Department of Pediatrics, University of Tennessee College of Medicine–Chattanooga BranchErlanger Health SystemChattanoogaUSA

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