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Pediatric Radiology

, Volume 35, Issue 9, pp 914–917 | Cite as

An atypical case of segmental spinal dysgenesis

  • Elodie ZanaEmail author
  • François Chalard
  • Keyvan Mazda
  • Guy Sebag
Case Report

Abstract

Spinal segmental dysgenesis is a complex closed dysraphism. The diagnostic criteria are: lumbar or thoracolumbar vertebral dysgenesis causing kyphosis, focal spinal cord narrowing without exiting roots, deformity of the lower limbs and paraplegia or paraparesis. We present a newborn who showed atypical features of bifocal spinal cord narrowing, without any vertebral abnormality at the proximal level. This seems to be a variant of this rare entity, whose early diagnosis is important, as surgical stabilisation of the spine is required.

Keywords

Spine Congenital Spinal segmental dysgenesis Children 

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Copyright information

© Springer-Verlag 2005

Authors and Affiliations

  • Elodie Zana
    • 1
    Email author
  • François Chalard
    • 1
  • Keyvan Mazda
    • 2
  • Guy Sebag
    • 1
  1. 1.Department of Paediatric ImagingHôpital Robert DebréParisFrance
  2. 2.Department of Paediatric Orthopaedic SurgeryHôpital Robert DebréParisFrance

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