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Pediatric Radiology

, Volume 35, Issue 8, pp 815–818 | Cite as

Diffuse choroid plexus hyperplasia: an under-diagnosed cause of hydrocephalus in children?

  • Azian Abd. Aziz
  • Lee Coleman
  • Andrew Morokoff
  • Wirginia Maixner
Case Report

Abstract

Hydrocephalus is a common neurological disorder in children and the result of a variety of causes. However, with the advancement of imaging modalities, particularly MRI, previously reported rarer causes of hydrocephalus in children are now being more readily appreciated. We report an 11-year-old boy with diffuse villous hyperplasia of the choroid plexus. He had a ventriculo-peritoneal (VP) shunt in-situ and a prior diagnosis from infancy of congenital aqueduct stenosis as the cause of his hydrocephalus. His current presentation was with further shunt dysfunction. CT and MRI demonstrated enlarged choroid plexuses but did not confirm aqueduct stenosis. CSF overproduction was demonstrated from the externalized ventricular drain. The enlarged choroid plexuses were surgically resected and histology confirmed choroid plexus hyperplasia. Identification of choroid plexus hyperplasia is important since the neurosurgical management of hydrocephalus is not VP shunt insertion, but resection of the hyperplastic choroid plexus.

Keywords

Hydrocephalus Choroid plexus hyperplasia MRI Child 

Notes

Acknowledgements

We thank Dr. Yuen Chan and Dr. Beena Kumar from the Department of Pathology, The Royal Children’s Hospital, for providing the histological illustrations.

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Copyright information

© Springer-Verlag 2005

Authors and Affiliations

  • Azian Abd. Aziz
    • 1
  • Lee Coleman
    • 1
  • Andrew Morokoff
    • 2
  • Wirginia Maixner
    • 2
  1. 1.Department of Medical ImagingThe Royal Children’s Hospital MelbourneParkville, VictoriaAustralia
  2. 2.Department of NeurosurgeryThe Royal Children’s Hospital MelbourneParkvilleAustralia

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