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Pediatric Radiology

, Volume 35, Issue 3, pp 339–343 | Cite as

Colonic neuroendocrine carcinoma in a child

  • Omai Al SasiEmail author
  • Rajeev Sathiapalan
  • Ayman Rifai
  • Asthma Mahmoud Mohamed Tulbah
  • Ali Al-Mehaidib
  • Amani Kofide
  • Claes Hugosson
Case Report

Abstract

A 10-year-old boy with congenital immunodeficiency (X-linked agammaglobulinaemia) presented with loss of appetite and weight, right-sided abdominal pain, diarrhoea and low-grade fever. Radiological investigations with barium follow-through, CT, PET and octreotide scans revealed a primary caecal/ascending proximal colonic mass with liver and bony metastases. Urine screen for 5HIAA was positive. Percutaneous liver biopsy confirmed the diagnosis of neuroendocrine carcinoma. The radiological work-up and the usefulness of various imaging modalities in the diagnosis of this rare paediatric tumour are discussed. The PET scan demonstrated the primary tumour and the metastatic locations more vividly than the octreotide scan, which is currently considered to be the most specific imaging modality for neuroendocrine masses.

Keywords

Abdomen Neuroendocrine carcinoma Metastases CT PET Radionuclide imaging Octreotide Child 

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Copyright information

© Springer-Verlag 2004

Authors and Affiliations

  • Omai Al Sasi
    • 1
    Email author
  • Rajeev Sathiapalan
    • 2
  • Ayman Rifai
    • 1
  • Asthma Mahmoud Mohamed Tulbah
    • 3
  • Ali Al-Mehaidib
    • 4
  • Amani Kofide
    • 2
  • Claes Hugosson
    • 1
  1. 1.Department of Radiology, MBC#28King Faisal Specialist Hospital and Research CentreRiyadhSaudi Arabia
  2. 2.Department of Paediatric Haematology and OncologyKing Faisal Specialist Hospital and Research CentreRiyadhSaudi Arabia
  3. 3.Department of PathologyKing Faisal Specialist Hospital and Research CentreRiyadhSaudi Arabia
  4. 4.Department of PaediatricsKing Faisal Specialist Hospital and Research CentreRiyadhSaudi Arabia

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