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Pediatric Radiology

, Volume 34, Issue 11, pp 908–911 | Cite as

Congenital bilateral perisylvian syndrome with pituitary hypoplasia and ectopic neurohypophysis

  • Ensar YekelerEmail author
  • Meral Ozmen
  • Hakan Genchellac
  • Memduh Dursun
  • Gulden Acunas
Case Report

Abstract

Congenital bilateral perisylvian syndrome (CBPS) is a congenital neurological syndrome characterized by pseudobulbar palsy, cognitive deficits and bilateral perisylvian abnormalities observed on imaging. The described abnormality in CBPS is polymicrogyria located in the frontal, parietal, and/or occipital lobes. A few syndromes or abnormalities associated with this syndrome have been documented. Pituitary abnormalities are rare disorders. Association of CBPS with pituitary abnormalities has not been reported previously. In this case, a combination of bilateral perisylvian polymicrogyria with pituitary hypoplasia and ectopic neurohypophysis, caused by a possible single common insult, is presented.

Keywords

Brain Pituitary Congenital bilateral perisylvian syndrome MRI Child 

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Copyright information

© Springer-Verlag 2004

Authors and Affiliations

  • Ensar Yekeler
    • 1
    Email author
  • Meral Ozmen
    • 2
  • Hakan Genchellac
    • 1
  • Memduh Dursun
    • 1
  • Gulden Acunas
    • 1
  1. 1.Department of RadiologyIstanbul Faculty of MedicineIstanbulTurkey
  2. 2.Department of Paediatric NeurologyIstanbul Faculty of MedicineIstanbulTurkey

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