Pediatric Cardiology

, Volume 38, Issue 5, pp 886–892 | Cite as

The Lymphatic Circulation in Adaptations to the Fontan Circulation

  • Sabarinath Menon
  • Murthy Chennapragada
  • Shinya Ugaki
  • Gary F. Sholler
  • Julian Ayer
  • David S. WinlawEmail author
Review Article


Failing Fontan continues to be major problem for patients on the univentricular pathway. Failing Fontan is often complicated by chylothorax, plastic bronchitis and protein loosing enteropathy. The role of lymphatic circulation in Fontan circulation is still being researched. Newer imaging modalities give insight into the role of abnormal dilatation and retrograde flow in lymphatic channels post Fontan. Interventional strategies targeting abnormal lymphatic channels, provides an alternative management strategy for patients with failing Fontan. This review focuses on the role of lymphatic system in adaptations to Fontan circulation


Fontan Fontan failure Lymphatics Lymphatic disorders Congenital heart disease Single ventricle physiology 



This work is funded by the Fontan Partnership Grant; NHMRC 1076849.

Compliance with Ethical Standards

Conflict of interest

There are no conflicts of interest for all authors.


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Copyright information

© Springer Science+Business Media New York 2017

Authors and Affiliations

  • Sabarinath Menon
    • 1
    • 2
    • 3
  • Murthy Chennapragada
    • 3
    • 4
  • Shinya Ugaki
    • 1
    • 3
  • Gary F. Sholler
    • 1
    • 3
    • 4
  • Julian Ayer
    • 1
    • 3
    • 4
  • David S. Winlaw
    • 1
    • 3
    • 4
    Email author
  1. 1.The Heart Centre for ChildrenThe Children’s Hospital at WestmeadSydneyAustralia
  2. 2.Sree Chitra Tirunal Institute of Medical sciences and TechnologyThiruvananthapuramIndia
  3. 3.Sydney Children’s Hospital NetworkThe Children’s Hospital at WestmeadWestmeadAustralia
  4. 4.Discipline of Child and Adolescent Health, Sydney Medical SchoolUniversity of SydneyCamperdownAustralia

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