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Pediatric Cardiology

, Volume 34, Issue 8, pp 2034–2036 | Cite as

Rupture of Sinus of Valsalva Aneurysm With Aorto-Biventricular Fistulas and Right-Ventricular Outflow Tract Obstruction: A Unique Association

  • Samer I. Masri
  • Fadi F. Bitar
  • Mariam T. Arabi
  • Marianne N. Majdalani
  • Mounir Y. Obeid
  • Zohair Y. Al Halees
  • Karim A. DiabEmail author
Case Report

Abstract

Sinus of Valsalva aneurysms are a rare entity. Rupture of such aneurysms is a major cause of aortocardiac fistulas usually occurring between the right sinus of Valsalva and right cardiac chambers. We report an exceptional case of a ruptured congenital sinus of Valsalva aneurysm with fistulas involving both the right- and left-ventricular outflow tracts and causing RVOT obstruction. We also demonstrate the utility of computed tomography angiography and transesophageal echocardiography in diagnosing these fistulas.

Keywords

Rupture sinus of Valsalva aneurysm Aorto-ventricular fistula Right-ventricular outflow tract obstruction 

Supplementary material

246_2012_581_MOESM1_ESM.mov (879 kb)
Transthoracic echocardiogram with parasternal short-axis view demonstrating the fistula arising from the right coronary sinus and causing obstruction to the RVOT

TEE demonstrating the fistula between the aortic root and the right ventricle

TEE with color flow Doppler demonstrating the aorto-biventricular fistulas between the right coronary sinus and both ventricular outflow tracts

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Copyright information

© Springer Science+Business Media New York 2012

Authors and Affiliations

  • Samer I. Masri
    • 1
  • Fadi F. Bitar
    • 1
  • Mariam T. Arabi
    • 1
  • Marianne N. Majdalani
    • 2
  • Mounir Y. Obeid
    • 1
    • 3
  • Zohair Y. Al Halees
    • 1
    • 3
    • 4
  • Karim A. Diab
    • 1
    Email author
  1. 1.Division of Pediatric Cardiology, Department of Pediatrics, Children’s Heart CenterAmerican University of Beirut Medical CenterBeirutLebanon
  2. 2.Division of Pediatric Intensive Care, Department of Pediatrics and Adolescent MedicineAmerican University of Beirut Medical CenterBeirutLebanon
  3. 3.Division of Cardiothoracic SurgeryAmerican University of Beirut Medical CenterBeirutLebanon
  4. 4.The Heart CenterKing Faisal Specialist Hospital and Research CenterRiyadhSaudi Arabia

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