Isolated cleft mitral valve (ICMV) is a rare entity not known to be related to pulmonary atresia with ventricular septal defect (PA-VSD). This report describes the use of cardiovascular magnetic resonance (CMR) imaging to diagnose ICMV in a patient with repaired PA-VSD who presented with incidental severe mitral regurgitation (MR) on follow-up echocardiography. An associated pulmonary varix secondary to the severe MR also was shown by CMR.
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Teo, L.L.S., Hia, C.P.P., Ling, L.H. et al. Isolated Cleft Mitral Valve With Severe Regurgitation Resulting in a Left Inferior Pulmonary Vein Varix Diagnosed From Cardiovascular Magnetic Resonance Imaging. Pediatr Cardiol 34, 1055–1056 (2013). https://doi.org/10.1007/s00246-012-0573-4
- Isolated cleft mitral valve
- Mitral regurgitation
- Pulmonary atresia
- Pulmonary varix
- Ventricular septal defect