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Pediatric Cardiology

, Volume 34, Issue 8, pp 1941–1944 | Cite as

Double-Outlet Right Ventricle Without Interventricular Communication: An Unusual and Challenging Problem

  • Mohit Singla
  • Osman Al-Radi
  • Luc MertensEmail author
Case Report

Abstract

A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy and clinical management of the patient is discussed together with an overview of the existing literature.

Keywords

Congenital heart disease Double-outlet right ventricle Rare defects 

Supplementary material

Supplementary movie S1 Color subcostal long-axis sweep demonstrating the origin of the aorta and the pulmonary artery from the right ventricle and the lack of any obvious interventricular communication. Also, the arrangement of the outflow tracts is shown. (AVI 33992 kb)

246_2012_483_MOESM2_ESM.avi (3.3 mb)
Supplementary movie S2 Color apical four-chamber view showing a thickened and dysplastic mitral valve with severe regurgitation and no ventriculoseptal defect (VSD). (AVI 3344 kb)

References

  1. 1.
    Accorsi F, Thiene G (1985) Double-outlet right ventricle with intact interventricular septum: case report, review of the literature, and proposed pathogenetic interpretation. G Ital Cardiol 15:232–237PubMedGoogle Scholar
  2. 2.
    Cavalini JF, Aiello VD, Guedes de Souza P, Trevisan IV, Marcial MB, Ebaid M (1998) Double-outlet right ventricle with intact atrial septum and restrictive ventricular septal defect: an analysis of two cases. Pediatr Cardiol 19:490–494CrossRefPubMedGoogle Scholar
  3. 3.
    Pace Napoleone C, Formigari R, Chiappini B, Frascaroli G, Gargiulo G (2003) Surgical management of double-outlet right ventricle with intact ventricular septum. Ann Thorac Surg 75:586–587CrossRefPubMedGoogle Scholar
  4. 4.
    Troise DE, Ranieri L, Arciprete PM (2001) Surgical repair for double-outlet right ventricle and intact ventricular septum. Ann Thorac Surg 71:1018–1019CrossRefPubMedGoogle Scholar
  5. 5.
    Troise DE, Ranieri L, Arciprete PM (2005) Optimal surgical repair for double-outlet right ventricle and intact ventricular septum. Ann Thorac Surg 79:1824 author reply 1824CrossRefPubMedGoogle Scholar
  6. 6.
    Vairo U, Tagliente MR, Fasano ML, Adurno G, Serino W (2001) Double-outlet right ventricle with intact ventricular septum. Ital Heart J 2:397–400PubMedGoogle Scholar

Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  1. 1.CardiologyThe Labatt Family Heart Centre, The Hospital for Sick ChildrenTorontoCanada

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