Double-Outlet Right Ventricle Without Interventricular Communication: An Unusual and Challenging Problem
- 215 Downloads
A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy and clinical management of the patient is discussed together with an overview of the existing literature.
KeywordsCongenital heart disease Double-outlet right ventricle Rare defects
Supplementary movie S1 Color subcostal long-axis sweep demonstrating the origin of the aorta and the pulmonary artery from the right ventricle and the lack of any obvious interventricular communication. Also, the arrangement of the outflow tracts is shown. (AVI 33992 kb)