Pediatric Cardiology

, Volume 34, Issue 8, pp 1877–1881 | Cite as

First Description of Coronary Artery Ostial Atresia With Fistulous Origin From a Normal Right Ventricle

  • Olawale OlabiyiEmail author
  • Debra Kearney
  • Rajesh Krishnamurthy
  • David Morales
  • Antonio G. Cabrera
Case Report


Anomalous origins of both the left and right coronary arteries are rare but have been well documented when both arteries arise from the pulmonary trunk (Angelini et al., Circulation 105:2449–2454, 2002). An anomalous coronary arterial origin from the pulmonary arteries usually involves the left coronary artery (ALCPA) and less frequently the right coronary artery (ARCPA). At least three cases have been reported in which the right coronary artery arose abnormally from the left ventricle (LV), but none have been reported in which both coronary arteries took their origin from the right ventricle (Ippisch and Kimball, J Am Soc Echocardiogr 23:222.e1–222.e2, 2010; Okuyama et al., Jpn Heart J 36:115–118, 1995; Culbertson et al., Pediatr Cardiol 16:73–75, 1995). Ostial atresia with anomalous origin of a coronary artery from the right ventricle has been described only in pulmonary atresia with an intact ventricular septum and a hypoplastic right ventricle. In this setting, atresia of both coronary ostia with right ventricular origin of both coronary arteries is a rare variant. This report presents a neonate in whom the entire coronary arterial system arose from the right ventricle via a single fistula with no other intracardiac defects. To the authors’ knowledge, this anomaly has not been described previously.


Anomalous coronary origin Coronary from right ventricle Coronary ostial atresia Myocardial ischemia Right ventricular fistula 

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Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Olawale Olabiyi
    • 1
    Email author
  • Debra Kearney
    • 2
  • Rajesh Krishnamurthy
    • 3
  • David Morales
    • 4
  • Antonio G. Cabrera
    • 1
  1. 1.Lillie Frank Abercrombie Section of Pediatric CardiologyTexas Children’s Hospital, Baylor College of MedicineHoustonUSA
  2. 2.Department of Pathology and ImmunologyTexas Children’s Hospital, Baylor College of MedicineHoustonUSA
  3. 3.Division of RadiologyTexas Children’s Hospital, Baylor College of MedicineHoustonUSA
  4. 4.Division of Cardiothoracic SurgeryTexas Children’s Hospital, Baylor College of MedicineHoustonUSA

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