The absence of a right superior vena cava (SVC) in situs solitus is very rare, and even then it is usually associated with left SVC. There have been few case reports in the literature of isolated bilateral absence of SVC. Bilateral absent SVC can have clinical implication, including pacemaker placements, central venous line placement, monitoring, and occasionally associated anomalies. We describe a case detected on fetal echocardiogram with bilateral absent SVC and structurally normal heart.
Superior vena cava Congenital heart disease Fetal echocardiography
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Movie 1. Fetal echocardogram showing the azygous vein connecting to the IVC. (MOV 742 kb)
Movie 2. Postnatal echocardiogram showing the connection of azygous vein to the IVC. (MOV 209 kb)
Movie 3. Postnatal echocardiogram with color showing the connection of azygous vein to the IVC. (MOV 332 kb)
Movie 4. CT angiogram showing both the azygous and hemiazygous veins joining together to drain into the IVC. (MOV 754 kb)
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