Pediatric Cardiology

, Volume 34, Issue 4, pp 1031–1033 | Cite as

Bilateral Absence of Superior Vena Cava

  • Manish BansalEmail author
  • James Strainic
  • Ravi Ashwath
Case Report


The absence of a right superior vena cava (SVC) in situs solitus is very rare, and even then it is usually associated with left SVC. There have been few case reports in the literature of isolated bilateral absence of SVC. Bilateral absent SVC can have clinical implication, including pacemaker placements, central venous line placement, monitoring, and occasionally associated anomalies. We describe a case detected on fetal echocardiogram with bilateral absent SVC and structurally normal heart.


Superior vena cava Congenital heart disease Fetal echocardiography 

Supplementary material

Movie 1. Fetal echocardogram showing the azygous vein connecting to the IVC. (MOV 742 kb)

Movie 2. Postnatal echocardiogram showing the connection of azygous vein to the IVC. (MOV 209 kb)

Movie 3. Postnatal echocardiogram with color showing the connection of azygous vein to the IVC. (MOV 332 kb) (754 kb)
Movie 4. CT angiogram showing both the azygous and hemiazygous veins joining together to drain into the IVC. (MOV 754 kb)


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Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  1. 1.Division of Pediatric Cardiology, Rainbow Babies and Children’s HospitalUniversity Hospitals Case Medical CenterClevelandUSA

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