An 11-month-old boy with a functionally single ventricle, coronary sinus ostial atresia, and bilateral superior vena cava (SVC) underwent coronary sinus unroofing upon a right bidirectional cavopulmonary shunt. A persistent left SVC left open to guarantee dual coronary venous drainage became dilated with cephalocaudal blood flow reversal and desaturation. The left SVC was surgically ligated on postoperative day 35.
Coronary sinus Functionally single ventricle Unroofing
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Movie clip 1. Preoperative echocardiogram showing a small vertical vein connected to the coronary sinus (CS) and draining to the innominate vein with blood flow in a caudocephalic direction (see redcolor-Doppler). (MOV 691 kb)
Movie clip 2. Postoperative echocardiogram showing a dilated left superior vena cava and blood flow in a cephalocaudal direction (see blue color-Doppler). (MOV 421 kb)
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