Pediatric Cardiology

, Volume 34, Issue 4, pp 1024–1026 | Cite as

Coronary Sinus Ostial Atresia Associated With Functionally Single Ventricle: Persistent Left Superior Vena Cava Should Be Ligated Upon Coronary Sinus Unroofing and Bidirectional Glenn Shunt

  • Hyung-Tae Sim
  • Jung-Jin Yu
  • Hyun-Woo Goo
  • Tae-Jin YunEmail author
Case Report


An 11-month-old boy with a functionally single ventricle, coronary sinus ostial atresia, and bilateral superior vena cava (SVC) underwent coronary sinus unroofing upon a right bidirectional cavopulmonary shunt. A persistent left SVC left open to guarantee dual coronary venous drainage became dilated with cephalocaudal blood flow reversal and desaturation. The left SVC was surgically ligated on postoperative day 35.


Coronary sinus Functionally single ventricle Unroofing 

Supplementary material

Movie clip 1. Preoperative echocardiogram showing a small vertical vein connected to the coronary sinus (CS) and draining to the innominate vein with blood flow in a caudocephalic direction (see red color-Doppler). (MOV 691 kb)

Movie clip 2. Postoperative echocardiogram showing a dilated left superior vena cava and blood flow in a cephalocaudal direction (see blue color-Doppler). (MOV 421 kb)


  1. 1.
    Kaneko Y, Kobayashi J, Yamamoto Y, Tsuchiya K (2008) Light-guided surgery to repair coronary sinus orifice atresia with left superior vena cava. Eur J Cardiothorac Surg 33:939–941PubMedCrossRefGoogle Scholar
  2. 2.
    Ohta N, Sakamoto K, Kado M, Nishioka M, Yokota M (2002) Surgical treatment of coronary sinus orifice atresia with hypoplastic left heart syndrome after total cavopulmonary connection. Ann Thorac Surg 73:653–655PubMedCrossRefGoogle Scholar
  3. 3.
    Oshima Y, Doi Y, Misaki T, Ichida F (2005) Surgical repair of coronary sinus orifice atresia. Eur J Cardiothorac Surg 27:351–352PubMedCrossRefGoogle Scholar
  4. 4.
    Salminen JT, Hakala T, Pihkala J, Mattila I, Puntila J, Sairanen H (2006) Coronary sinus orifice atresia with left superior vena cava in patients with univentricular heart. Ann Thorac Surg 81:e16–e17PubMedCrossRefGoogle Scholar
  5. 5.
    Santoscoy R, Walter H, Ross DR, Lyons JM, Hakimi M (1996) Coronary sinus ostial atresia with persistent left superior vena cava. Ann Thorac Surg 61:879–882PubMedCrossRefGoogle Scholar

Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Hyung-Tae Sim
    • 1
  • Jung-Jin Yu
    • 2
  • Hyun-Woo Goo
    • 3
  • Tae-Jin Yun
    • 1
    Email author
  1. 1.Division of Pediatric Cardiac Surgery, Asan Medical Center, College of MedicineUniversity of UlsanSeoulRepublic of Korea
  2. 2.Division of Pediatric Cardiology, Asan Medical Center, College of MedicineUniversity of UlsanSeoulRepublic of Korea
  3. 3.Department of Radiology, Asan Medical Center, College of MedicineUniversity of UlsanSeoulRepublic of Korea

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