Pediatric Cardiology

, Volume 33, Issue 5, pp 869–871

Neonatal Midaortic Syndrome and Renal Artery Atresia Presenting as Malignant Hypertension

  • Tal A. Gospin
  • Jarrod D. Knudson
  • Christopher J. Petit
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Abstract

We report a case of congenital midaortic syndrome with bilateral renal artery atresia in a premature female neonate born by way of caesarean section secondary to acute onset of decreased fetal movement and polyhydramnios. The infant required cardiopulmonary resuscitation at birth, and initial echocardiogram exhibited normal intracardiac anatomy and mildly depressed left-ventricular systolic function. Within 24 h, the neonate developed severe systemic arterial hypertension and acute renal failure. Ultrasound demonstrated hyperechoic kidneys and a hypoplastic abdominal aorta. Angiography revealed severe suprarenal hypoplasia of the abdominal aorta with bilateral renal artery atresia. Medical support was withdrawn, and the patient died shortly thereafter.

Keywords

Midaortic syndrome Neonatal hypertension Renal artery atresia Abdominal coarctation 

Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Tal A. Gospin
    • 1
  • Jarrod D. Knudson
    • 1
  • Christopher J. Petit
    • 1
  1. 1.Division of Pediatric Cardiology, Department of PediatricsBaylor College of Medicine/Texas Children’s HospitalHoustonUSA

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