Pediatric Cardiology

, Volume 33, Issue 7, pp 1190–1195 | Cite as

Complete Transposition of Great Arteries with Cor Triatriatum: An Unusual Coexistence

  • Saurabh Kumar Gupta
  • Anita SaxenaEmail author
  • S. Ramakrishnan
  • Rajneesh Juneja
  • V. Devagourou
Case Report


The combination of complete transposition of the great arteries and cor triatriatum is extremely rare. We report three infants with this rare combination and discuss the anatomic details apparently unique to the combined lesion.


Transposition of great arteries Cor triatriatum Echocardiography 

Supplementary material

Video 1 Apical four-chamber view with anterior tilt from case no. 1 showing ventriculo-arterial discordance and VSD in the muscular septum flowing right to left (AVI 527 kb)

Video 2 Apical four-chamber view with colour Doppler from case no. 1 showing turbulence across the membrane in the LA, mild MR, and moderate tricuspid regurgitation (AVI 415 kb)

Video 3 Apical four-chamber view with colour Doppler from case no. 2 showing the upper muscular VSD flowing right to left and the ASD flowing left to right (AVI 677 kb)


  1. 1.
    Binotto M, Aiello V, Ebaid M (1997) Coexistence of divided left atrium (cor triatriatum) and tetralogy of Fallot. J Thorac Cardiovasc Surg 45:92–95Google Scholar
  2. 2.
    Goel AK, Saxena A, Kothari SS (1998) Atrioventricular septal defect with cor triatriatum: case report and review of the literature. Pediatr Cardiol 19:243–245PubMedCrossRefGoogle Scholar
  3. 3.
    Jayranganath M, Subramanian Anand, Manjunath CN (2011) Congenitally corrected transposition of the great arteries in a patient with cor triatriatum: a rare combination. Pediatr Cardiol 32:515–517PubMedCrossRefGoogle Scholar
  4. 4.
    Keith JD (1978) Prevalence, incidence and epidemiology. In: Keith JD, Rowe RD, Vlad P (eds) Heart disease in infancy and children, 3rd edn. Macmillan, New York, pp 3–13Google Scholar
  5. 5.
    Lam CR, Green E, Drake E (1962) Diagnosis and surgical correction of 2 types of triatrial heart. Surgery 51:127–137Google Scholar
  6. 6.
    Marin-Garcia J, Tandon R et al (1975) Cor triatriatum: study of 20 cases. Am J Cardiol 35:59–66PubMedCrossRefGoogle Scholar
  7. 7.
    Oglietti J, Cooley DA et al (1983) Cor triatriatum: operative results in 25 patients. Ann Thorac Surg 35:415–420PubMedCrossRefGoogle Scholar
  8. 8.
    Samanek M, Voriskova M (1999) Congenital heart disease among 815,569 children born between 1980 and 1989 and their 15 year survival: a prospective Bohemia survival study. Pediatr Cardiol 20:411–417PubMedCrossRefGoogle Scholar
  9. 9.
    Thies WR, Mathies W, Minami K, Pott U, Meyer H, Korfer R (1990) Surgical repair and postoperative course of an infant with infracardiac total anomalous pulmonary venous connection, cor triatriatum sinistrum and transposition of the great arteries. Eur J Cardiothorac Surg 4:45–47PubMedCrossRefGoogle Scholar
  10. 10.
    Vernovsky G (2008) Transposition of great arteries. In: Allen HD, Driscoll DJ, Shaddy RE, Feltes TF (eds) Moss and Adams’ heart disease in infants, children, and adolescent: including the fetus and young adults, 7th edn. Wolter Kluwer, Netherlands, pp 1038–1087Google Scholar

Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Saurabh Kumar Gupta
    • 1
  • Anita Saxena
    • 1
    Email author
  • S. Ramakrishnan
    • 1
  • Rajneesh Juneja
    • 1
  • V. Devagourou
    • 2
  1. 1.Department of CardiologyAll India Institute of Medical SciencesNew DelhiIndia
  2. 2.Department of Cardiovascular & Thoracic SurgeryAll India Institute of Medical SciencesNew DelhiIndia

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