Cor Triatriatum With Partial Anomalous Pulmonary Venous Return: A Rare Case of Parallel Obstruction and Successful Staged Treatment
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Cor triatriatum sinister is an uncommon congenital cardiac defect that has rarely been described in association with left-sided partial anomalous pulmonary venous return. We present a case of such rare anatomy with multilevel obstruction that presented in infancy as cardiogenic shock. The patient underwent staged treatment with extracorporeal membrane oxygenation stabilization, catheter-based balloon dilatation of the cor triatriatum and atrial septostomy, followed by definitive surgical repair, with excellent result.
KeywordsCor triatriatum Partial anomalous pulmonary venous return Pulmonary venous obstruction Cardiac catheterization Cardiac surgery
A subcostal long-axis echocardiographic clip shows a large, tense cor chamber in the left atrium; a compressed true left atrium; a dilated right ventricle; and an underfilled left ventricle. Left-ventricular diastolic compression is indicative of right-ventricular volume overload. (AVI 5453 kb)
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