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Pediatric Cardiology

, Volume 33, Issue 2, pp 363–365 | Cite as

Cor Triatriatum With Partial Anomalous Pulmonary Venous Return: A Rare Case of Parallel Obstruction and Successful Staged Treatment

  • Ofer SchillerEmail author
  • Kristin M. Burns
  • Pranava Sinha
  • Susan D. Cummings
Case Report

Abstract

Cor triatriatum sinister is an uncommon congenital cardiac defect that has rarely been described in association with left-sided partial anomalous pulmonary venous return. We present a case of such rare anatomy with multilevel obstruction that presented in infancy as cardiogenic shock. The patient underwent staged treatment with extracorporeal membrane oxygenation stabilization, catheter-based balloon dilatation of the cor triatriatum and atrial septostomy, followed by definitive surgical repair, with excellent result.

Keywords

Cor triatriatum Partial anomalous pulmonary venous return Pulmonary venous obstruction Cardiac catheterization Cardiac surgery 

Supplementary material

A subcostal long-axis echocardiographic clip shows a large, tense cor chamber in the left atrium; a compressed true left atrium; a dilated right ventricle; and an underfilled left ventricle. Left-ventricular diastolic compression is indicative of right-ventricular volume overload. (AVI 5453 kb)

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A subcostal color echocardiographic clip shows increased right superior vena cava flow (red jet at the left side of the color box), right-to-left atrial level shunting (blue jet), and flow from the cor chamber to the true left atrium (red jet at the center of the color box). (AVI 2246 kb)
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Right lower pulmonary vein angiography shows drainage of the right pulmonary veins into a large, tense cor chamber with little blood egress to the left ventricle. The true left atrium is compressed by the cor chamber. (AVI 2440 kb)
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Right lower pulmonary vein angiography after balloon dilation of the cor membrane orifice. The cor chamber is smaller, there is less compression of the true left atrium, and blood flow to the left ventricle is significantly increased. (AVI 1966 kb)

References

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Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  • Ofer Schiller
    • 1
    Email author
  • Kristin M. Burns
    • 1
  • Pranava Sinha
    • 2
  • Susan D. Cummings
    • 1
  1. 1.Division of CardiologyChildren’s National Medical CenterWashingtonUSA
  2. 2.Department of Cardiovascular SurgeryChildren’s National Medical CenterWashingtonUSA

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