Pediatric Cardiology

, Volume 32, Issue 7, pp 990–992 | Cite as

Aortic Intimal Fold in Takayasu Arteritis Causing Obstruction of Left Coronary Ostium

  • Masakazu NakaoEmail author
  • Kim-Kiat Ong
  • Yeong-Phang Lim
  • Keng-Yean Wong
Case Report


An 11-year-old girl with Takayasu arteritis was presented with recurrent chest pain. A transthoracic echocardiogram showed moderate to severe aortic regurgitation with impaired cardiac function. Cardiac catheterization revealed the total occlusion of the small right coronary artery and left main stenosis of 40%. An intraoperative transesophageal echocardiogram showed a redundant intimal fold partially covering the left coronary ostium and this was further confirmed from the intraoperative finding. This is a case report of recurrent angina associated with obstruction of left main coronary artery orifice by an intimal fold secondary to Takayasu arteritis.


Intimal fold Takayasu arteritis Coronary obstruction 

Supplementary material

Movie clip 1 Intraoperative TEE uncovered the intimal fold partially obstructing the left coronary ostium. (MOV 747 kb)

Movie clip 2 Color-Doppler image of intraoperative TEE showing a turbulence along the left coronary ostium. (MOV 786 kb)


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Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  • Masakazu Nakao
    • 1
    Email author
  • Kim-Kiat Ong
    • 1
  • Yeong-Phang Lim
    • 1
    • 2
  • Keng-Yean Wong
    • 3
  1. 1.Cardiothoracic Service, Division of SurgeryKK Women’s and Children’s HospitalSingaporeSingapore
  2. 2.Department of Cardiothoracic SurgeryNational Heart Centre SingaporeSingaporeSingapore
  3. 3.Cardiology Service, Department of Pediatric SubspecialtiesKK Women’s and Children’s HospitalSingaporeSingapore

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