Pediatric Cardiology

, Volume 32, Issue 2, pp 221–223 | Cite as

Primary Repair of Aortopulmonary Window with an Interrupted Aortic Arch in a Very Low-Birth-Weight Premature Neonate

  • Toru OkamuraEmail author
  • Mitsugi Nagashima
  • Fumiaki Shikata
Case Report


The aortopulmonary window concomitant with an interrupted aortic arch is a rare occurrence. We successfully performed an emergency one-stage surgical repair of the aortopulmonary window (type 1) concomitant with an interrupted aortic arch (type A) in the case of a very low-birth-weight (1230-g) premature 2-day-old neonate. We describe the diagnosis, surgery, and postoperative course of this rare occurrence.


Aortopulmonary window Interrupted aortic arch Low-birth-weight premature baby 


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Copyright information

© Springer Science+Business Media, LLC 2010

Authors and Affiliations

  • Toru Okamura
    • 1
    Email author
  • Mitsugi Nagashima
    • 1
  • Fumiaki Shikata
    • 1
  1. 1.Cardiovascular Surgery, School of MedicineEhime University ShitukawaToon CityJapan

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