Pediatric Cardiology

, Volume 31, Issue 4, pp 534–537 | Cite as

Left Hemitruncus Associated with Tetralogy of Fallot: Fetal Diagnosis and Postnatal Echocardiographic and Cardiac Computed Tomographic Confirmation

  • Karim Diab
  • Randy Richardson
  • Stephen Pophal
  • Ernerio Alboliras
Case Report
First Online:
Received:
Accepted:

Abstract

Anomalous origin of one pulmonary artery from the aorta, or hemitruncus, is a rare cardiac malformation. We report a case of left hemitruncus (aortic origin of the left pulmonary artery) associated with tetralogy of Fallot diagnosed in utero. To the authors’ knowledge, this is the first such case diagnosed by fetal echocardiography to be described in the literature. The condition was documented by postnatal echocardiogram and cardiac computed tomography. Prompt recognition of this lesion is essential for early repair to improve outcome.

Keywords

Cardiac computed tomography Fetal echocardiography Hemitruncus Tetralogy of Fallot 
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Copyright information

© Springer Science+Business Media, LLC 2009

Authors and Affiliations

  • Karim Diab
    • 1
  • Randy Richardson
    • 2
  • Stephen Pophal
    • 1
  • Ernerio Alboliras
    • 1
  1. 1.Department of Pediatrics, Scott and Laura Eller Congenital Heart CenterSt. Joseph Hospital and Medical CenterPhoenixUSA
  2. 2.Department of RadiologySt. Joseph Hospital and Medical CenterPhoenixUSA

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