The commonly used Darling classification for total anomalous pulmonary venous connection (TAPVC) consists of supracardiac, cardiac, infracardiac, and mixed types (Craig et al., Lab Invest 6:44–64, 1967). In supracardiac TAPVC, the common pulmonary vein drains superiorly into the left innominate vein, the superior vena cava, or the azygos vein by way of an ascending vertical vein. We describe a case of supracardiac TAPVC draining into the azygos vein atypically by way of a descending vertical vein.
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Craig JM, Darling RC, Rothney WB (1957) Total pulmonary venous drainage into the right side of the heart: Report of 17 autopsied cases not associated with other major cardiovascular anomalies. Lab Invest 6:44–64
Edward JE (1953) Pathologic and developmental considerations in anomalous pulmonary venous connection. Proc Staff Meet Mayo Clin 28:441–452
Moes CAF, Fowler RS, Trusler GA (1966) Total anomalous pulmonary venous drainage into the azygous vein. Am J Roentgenol 98:378–387
Musolino AM, Santora G, Marino B, Formigari R, Guccione P, Pasquini L (1999) Echocardiographic diagnosis of totally anomalous pulmonary venous connection to the azygous vein. Cardiol Young 9:305–309
Tomar M, Radhakrishnan S, Iyer KS, Shrivastava S (2006) Total anomalous pulmonary venous connection to azygous vein: Echocardiographic recognition of a rare variant. Ind Heart J 58:54–56
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Video 1 Suprasternal view on color Doppler echocardiogram showing right upper and lower pulmonary veins draining into a common confluence which is coursing toward the left across the midline, turning inferiorly to form a descending vertical vein into which the left upper and lower veins are seen draining. This descending vertical vein is then seen crossing the midline to drain into the azygos vein where it is narrowed in caliber. The azygos vein is then seen coursing superiorly on the right side. (MOV 2,324 kb)
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Shah, S., Singh, M., John, C. et al. Supracardiac Total Anomalous Pulmonary Venous Connection with A Descending Vertical Vein. Pediatr Cardiol 30, 1043–1045 (2009) doi:10.1007/s00246-009-9509-z
- Congenital heart disease
- Total anomalous pulmonary venous connection