Pediatric Cardiology

, Volume 29, Issue 4, pp 862–864 | Cite as

Isolated Congenital Absence of the Pericardium

  • Ayse Murat
  • Hakan ArtasEmail author
  • Erdal Yilmaz
  • Erkin Ogur
Images in Pediatric Cardiology


Absence of the pericardium can vary from partial to complete absence. Patients with complete absence of the pericardium are either asymptomatic or have nonspecific chest pain, and no treatment is needed. Patients with partial absence of the pericardium are at risk for possible symptomatic herniation of the left atrial appendage or left ventricle, leading to fatal myocardial strangulation. Therefore, it is very important to differentiate partial from complete absence of the pericardium. A 7-year-old girl presented with isolated congenital absence of the pericardium, which generally has a good prognosis. It is a relatively asymptomatic anomaly that usually requires no treatment. Some cases involve complications that require operative treatment. Absence of the pericardium can be precisely defined by computed tomography and magnetic resonance imaging.


Chest x-ray Magnetic resonance Pericardium 


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Copyright information

© Springer Science+Business Media, LLC 2008

Authors and Affiliations

  • Ayse Murat
    • 1
  • Hakan Artas
    • 2
    Email author
  • Erdal Yilmaz
    • 3
  • Erkin Ogur
    • 1
  1. 1.Department of Radiology, Faculty of MedicineFırat UniversityElazigTurkey
  2. 2.Department of RadiologyElazıg Training and Research HospitalElazigTurkey
  3. 3.Department of Pediatrics, Division of Pediatric Cardiology, Faculty of MedicineFirat UniversityElazigTurkey

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