Pediatric Cardiology

, Volume 29, Issue 5, pp 976–979

Bronchoscopic Diagnosis of Asymptomatic Unilateral Pulmonary Vein Atresia in an Infant

  • Cécile Tissot
  • Regula Corbelli
  • Yacine Aggoun
  • Maurice Beghetti
  • Eduardo da Cruz
Case Report

Abstract

An eight-month-old boy with findings of persistent left pulmonary basal infiltrate was diagnosed with congenital unilateral pulmonary vein atresia by bronchoscopy. Cardiac catheterization documented slow left pulmonary venous return to atretic pulmonary veins. Conservative treatment was chosen because the child was asymptomatic and corrective surgery or percutaneous intervention was not technically possible. After a 3-year follow-up, the child still has no documented pulmonary hypertension. Early diagnosis of unilateral pulmonary vein atresia is important to anticipate potential threatening complications like pulmonary hypertension and hemoptysis. Surgical treatment of this entity might be drastic and complex and should be weighed against a conservative alternative and careful follow-up.

Keywords

Pulmonary vein atresia Pulmonary hypertension Hemoptysis Children 

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Copyright information

© Springer Science+Business Media, LLC 2007

Authors and Affiliations

  • Cécile Tissot
    • 1
  • Regula Corbelli
    • 2
  • Yacine Aggoun
    • 3
  • Maurice Beghetti
    • 3
  • Eduardo da Cruz
    • 1
  1. 1.The Heart Institute, Department of Pediatrics, The Children’s Hospital of DenverUniversity of Colorado at Denver & Health Sciences CenterDenverUSA
  2. 2.Pediatric Pulmonology Unit, Department of PediatricsChildren’s University Hospital of GenevaGenevaSwitzerland
  3. 3.Pediatric Cardiology Unit, Department of PediatricsChildren’s University Hospital of GenevaGenevaSwitzerland

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