Bronchoscopic Diagnosis of Asymptomatic Unilateral Pulmonary Vein Atresia in an Infant
- 108 Downloads
An eight-month-old boy with findings of persistent left pulmonary basal infiltrate was diagnosed with congenital unilateral pulmonary vein atresia by bronchoscopy. Cardiac catheterization documented slow left pulmonary venous return to atretic pulmonary veins. Conservative treatment was chosen because the child was asymptomatic and corrective surgery or percutaneous intervention was not technically possible. After a 3-year follow-up, the child still has no documented pulmonary hypertension. Early diagnosis of unilateral pulmonary vein atresia is important to anticipate potential threatening complications like pulmonary hypertension and hemoptysis. Surgical treatment of this entity might be drastic and complex and should be weighed against a conservative alternative and careful follow-up.
KeywordsPulmonary vein atresia Pulmonary hypertension Hemoptysis Children
The authors would like to thank Constance Barazzone, MD, for her support in the follow-up of this patient.
- 3.Edwards JE (1960) Congenital stenosis of pulmonary veins. Pathologic and developmental considerations. Lab Invest 9:46–66Google Scholar
- 4.vHeyneman LE, Nolan RL, Harrison JK, McAdams HP (2001) Congenital unilateral pulmonary vein atresia: radiologic findings in three adult patients. Am J Roentgenol 177:681–685Google Scholar
- 6.Lacour-Gayet F (2006) Surgery for pulmonary venous obstruction after repair of total anomalous pulmonary venous return. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 45–50. ReviewGoogle Scholar