Pediatric Cardiology

, Volume 29, Issue 2, pp 434–437 | Cite as

Anomalous Left Coronary Artery from the Right Sinus of Valsalva and Noncompaction of the Left Ventricle

  • Katheryn Gambetta
  • Wei Cui
  • Chawki el-Zein
  • David A. Roberson
Case Report


Anomalous origin of the left coronary artery is a well-known cause of sudden death. Noncompaction of the ventricular myocardium is a cardiomyopathy characterized by prominent trabeculae and deep intertrabecular recesses. Both anomalies are rare. We report the case of a child with both anomalous origin of the left coronary artery from the right sinus of Valsalva and noncompaction of the left ventricular myocardium found during an evaluation for Kawasaki’s disease.


Anomalous origin of left coronary artery Noncompaction of ventricular myocardium Kawasaki’s disease 


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Copyright information

© Springer Science+Business Media, LLC 2007

Authors and Affiliations

  • Katheryn Gambetta
    • 1
  • Wei Cui
    • 1
  • Chawki el-Zein
    • 1
  • David A. Roberson
    • 1
  1. 1.The Heart Institute for ChildrenHope Children’s HospitalOaklawnUSA

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