Pediatric Cardiology

, Volume 27, Issue 6, pp 755–758 | Cite as

Surgical Correction of Mitral Valve Prolapse

A Cure for Recurrent Ventricular Tachycardia in Marfan Syndrome?
  • Rebecca S. Beroukhim
  • John H. Reed
  • Michael S. Schaffer
  • Anji T. Yetman
CASE REPORT
  • 101 Downloads

Abstract

We describe the case of a 3-year-old child with neonatal Marfan syndrome complicated by mitral valve prolapse with regurgitation, marked aortic root dilatation, and ventricular tachycardia. The patient had resolution of ventricular tachycardia following surgical intervention consisting of a valve-sparing aortic root replacement and mitral valve annuloplasty.

Keywords

Marfan Pediatric Tachycardia Mitral 

References

  1. 1.
    Chen S, Fagan LF, Nouri S, Donahoe JL (1985) Ventricular dysrhythmias in children with Marfan’s syndrome. Am J Dis Child 139:273–276PubMedGoogle Scholar
  2. 2.
    Chesler E, King RA, Edwards JE (1983) The myxomatous mitral valve and sudden death. Circulation 67:632–639PubMedGoogle Scholar
  3. 3.
    Cobbs BW Jr, King SB 3rd (1977) Ventricular buckling: a factor in the abnormal ventriculogram and peculiar hemodynamics associated with mitral valve prolapse. Am Heart J 93:741–758PubMedCrossRefGoogle Scholar
  4. 4.
    De Paepe A, Devereux RB, Dietz HC, Hennekam RG, Pyeritz RE (1996) Revised diagnostic criteria for the Marfan syndrome. Am J Med Genet 62:417–426PubMedCrossRefGoogle Scholar
  5. 5.
    Kavey RE, Blackman MS, Sondheimer HM, Byrum CJ (1984) Ventricular arrhythmias and mitral valve prolapse in childhood. J Pediatr 105:885–890PubMedCrossRefGoogle Scholar
  6. 6.
    Ross A, DeWeese JA, Yu PN (1978) Refractory ventricular arrhythmias in a patient with mitral valve prolapse. Successful control with mitral valve replacement. J Electrocardiol 11:289–295PubMedGoogle Scholar
  7. 7.
    Swartz MH, Teichholz LE, Donoso E (1977) Mitral valve prolapse: a review of associated arrhythmias. Am J Med 62:377–389PubMedCrossRefGoogle Scholar
  8. 8.
    Yetman AT, Bornemeier RA, McCrindle BW (2003) Long-term outcome in patients with Marfan syndrome: is aortic dissection the only cause of sudden death? J Am Coll Cardiol 41:329–332PubMedCrossRefGoogle Scholar

Copyright information

© Springer Science+Business Media, Inc. 2006

Authors and Affiliations

  • Rebecca S. Beroukhim
    • 1
  • John H. Reed
    • 1
  • Michael S. Schaffer
    • 1
  • Anji T. Yetman
    • 1
  1. 1.Children’s Hospital Heart Institute, University of Colorado Health Sciences Center & The Children’s HospitalDenverUSA

Personalised recommendations