Pediatric Cardiology

, Volume 27, Issue 3, pp 381–384 | Cite as

Enlarged Left Vitelline Vein Remnant as a Cause of Cyanosis after the Fontan Procedure: Resolution with an Amplatzer Vascular Plug

Article
First Online:

Abstract

A 6-year-old girl with heterotaxy and a functional single ventricle had persistent cyanosis 4 years after a fenestrated Fontan procedure. Cardiac catheterization revealed a large venous fistula from a left-sided hepatic vein to the coronary sinus, resulting in desaturation. The anomalous vein was occluded with an Amplatzer vascular plug.

Keywords

Cyanosis Fontan Venous collateral 
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Copyright information

© Springer Science+Business Media, Inc. 2006

Authors and Affiliations

  • A. Rothman
    • 1
  • R.J. Acherman
    • 1
  • C.F. Luna
    • 1
  • H. Restrepo
    • 1
  1. 1.Children’s Heart Center and the Department of PediatricsUniversity of Nevada School of MedicineLas VegasUSA

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