Pediatric Cardiology

, Volume 25, Issue 6, pp 675–676 | Cite as

Reversible Cardiomyopathy Caused by an Uncommon Form of Congenital Adrenal Hyperplasia



A child with 11, β-hydroxylase deficiency, an unusual variant of congenital adrenal hyperplasia, presented with dilated cardiomyopathy. Congestive heart failure and dilatation of ventricles resolved with hydrocortisone replacement therapy. This case highlights the importance of complete history and physical examination of children with dilated cardiomyopathy.


Dilated cardiomyopathy Congenital adrenal hyperplasia 


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Copyright information

© Springer-Verlag 2004

Authors and Affiliations

  1. 1.Department of PediatricsKing Khalid University HospitalRiyadhSaudi Arabia

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