Pediatric Cardiology

, Volume 25, Issue 1, pp 67–69 | Cite as

Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum

  • S. E. Selamet
  • D. T. Hsu
  • H. M. Thaker
  • W. M. Gersony
Article

Abstract

We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.

Keywords

Atresia of Coronary Ostia Pulmonary Atresia Ischemia Myocardial Infarction 

Notes

Acknowledgments

We thank Drs. Donald Leichter from the Division of Pediatric Cardiology and Melissa Gill from the Department of Pathology for their contributions.

References

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Copyright information

© Springer-Verlag 2003

Authors and Affiliations

  • S. E. Selamet
    • 1
  • D. T. Hsu
    • 1
  • H. M. Thaker
    • 2
  • W. M. Gersony
    • 1
  1. 1.Department of PediatricsCollege of Physicians and Surgeons, Columbia University, New York, NY 10032USA
  2. 2.Department of PathologyCollege of Physicians and Surgeons, Columbia University, New York, NY 10032USA

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