Pediatric Cardiology

, Volume 24, Issue 5, pp 498–502 | Cite as

A Case of Superoinferior Ventricular Heart with Situs Ambiguus, Dextroventricular Loop, and Levo Transposition of the Arteries

  • S. Özkutlu
  • C. AyabakanEmail author
  • M. Demircin
  • M. Yilmaz
Case Report


A unique case of superoinferior ventricles, left atrial isomerism, concordant atrioventricular connection, and discordant ventriculoarterial connection is described. The associated anomalies were azygous vein continuation, large subpulmonary and apical ventricular septal defects, and left ventricular outflow tract obstruction (pulmonary stenosis). The diagnosis was mostly made by fetal echocardiography and the superoinferior location of the ventricles was confirmed by postnatal echocardiography. Fetal and postnatal echocardiography facilitated the precise morphologic diagnosis and segmental analysis of this defect.


Echocardiography Superoinferior ventricles 


  1. 1.
    Alday, LE, Juaneda, E 1993Superoinferior ventricles with criss-cross atrioventricular connections and intact ventricular septum.Pediatr Cardiol14238241PubMedGoogle Scholar
  2. 2.
    Anderson, RH 1982A question of definition.Criss-cross hearts revised. Pediatr Cardiol3305313Google Scholar
  3. 3.
    Cordes, TM, O’Leary, PW, Seward, JB, Hagler, DJ 1994Distinguishing right from left: a standardized technique for fetal echocardiography.J Am Soc Echocardiogr74753PubMedGoogle Scholar
  4. 4.
    Freedom, RM 1983Supero-inferior ventricle and criss-cross atrioventricular connections: an analysis of the myth and mystery.Modern Probl Pediatr224862Google Scholar
  5. 5.
    Freedom, RM, Culhman, G, Rowe, RD 1978The criss-cross and superoinferior ventricular heart: an angiographic study.Am J Cardiol42620628PubMedGoogle Scholar
  6. 6.
    Hery, E, Jimenez, M, Didier, D,  et al. 1989Echocardiographic and angiographic findings in superior–inferior cardiac ventricles.Am J Cardiol6313851389PubMedGoogle Scholar
  7. 7.
    Ozkutlu, S, Elshershari, H, Akcoren, Z, Onderoglu, LS, Tekinalp, G 2002Visceroatrial situs solitus with atrioventricular alignment discordance, double outlet right ventricle and superoinferior ventricles: fetal and neonatal echocardiographic findings.J Am Soc Echocardiogr15749752CrossRefPubMedGoogle Scholar
  8. 8.
    Ozkutlu, S, Saraclar, M 1999The accuracy of antenatal fetal echocardiography.Turk J Ped41349352Google Scholar
  9. 9.
    Santos, MA, Simoes, LC 1987Paroxysmal supraventricular tachycardia in supero-inferior ventricles with intact ventricular septum.Int J Cardiol14232235PubMedGoogle Scholar
  10. 10.
    Snider, RA, Serwer, GA, Ritter, SB 1997Specialized echocardiographic techniques.Snider, RASerwer, GARitter, SB eds. Echocardiography in Pediatric Heart DiseaseMosby-Year BookSt. Louis76133Google Scholar
  11. 11.
    Valdes-Cruz, LM, Cayre, RO 2000Superioinferior ventricles and crisscross heart.Valdes-Cruz, LMCayre, RO eds. Echocardiographic Diagnosis of Congenital Heart Disease. An Embryologic and Anatomic ApproachLippincott–RavenPhiladelphia289294Google Scholar
  12. 12.
    Van Praagh, S, La Corte, M, Fellows, KE 1980Supero-inferior ventricles: anatomic and angiocardiographic findings in ten postmortem cases.Van Praagh, RTokao, A eds. Etiology and Morphogenesis of Congenital Heart DiseaseFuturaNew York317378Google Scholar
  13. 13.
    Zach, M, Singer, H, Loser, H, Hagel, KJ,  et al. 1980The horizontal interventricular septum. Three cases with different ventriculoarterial connections.Eur J Cardiol11269282PubMedGoogle Scholar

Copyright information

© Springer-Verlag 2003

Authors and Affiliations

  • S. Özkutlu
    • 1
  • C. Ayabakan
    • 1
    Email author
  • M. Demircin
    • 1
  • M. Yilmaz
    • 1
  1. 1.Departments of Pediatric Cardiology and Thoracic and Cardiovascular SurgeryHacettepe University Ihsan Dogramaci Childern’s Hospital, 06100 AnkaraTurkey

Personalised recommendations