Giant primary lymphedema of the vulva in a young female
A 21-year-old single female with a large swelling of the vulva’s left labia majora was diagnosed with a case of primary lymphedema of the left lower limb and external genitalia. The giant labial swelling was excised, and the patient experiences no complications or recurrence for 7 months postoperatively. Following the surgical excision of the swelling, the left labia majora and minora were reconstructed successfully. The excised mass weighed 6.3 kg and measured 40 cm x 35 cm x 30 cm. There were no complications postoperatively, and the patient has not experienced recurrence during the 7-month follow-up period. The patient returned to her normal life.
Level of evidence: Level V, therapeutic study.
KeywordsPrimary lymphedema Giant swelling Vulva Labiaplasty
Compliance with ethical standards
Conflict of interest
All authors declare that they have no conflict of interest.
• The manuscript has not been submitted to any other journals for simultaneous consideration.
• The manuscript has not been published previously (partly or in full).
• No data have been fabricated or manipulated (including images) to support our conclusions
• No data, text, or theories by others are presented as if they were our own.
• Consent to submit has been received from all co-authors.
• Authors whose names appear on the submission have contributed sufficiently to the scientific work and therefore share collective responsibility and accountability for the results.
• All procedures performed in this study involving patient were in accordance with the ethical standards of the General Organization of Teaching Hospitals and Institutes (GOTHI) research committee.
• Informed consent was obtained from the patient herself for surgical intervention and also for publication of photos.
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