Introduction and hypothesis
Several reports have described vaginal prolapse in Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome patients after creation of a neovagina. To our knowledge, no reports of primary vaginal prolapse of a blind pouch without previous intervention, or surgery for this condition, have been described.
In this case report, we describe a 19-year-old woman with MRKH and complete prolapse of her shortened vaginal pouch. Surgical correction utilizing permanent suture-based sacrospinous ligament fixation was performed.
The patient had a successful outcome.
Sacrospinous ligament fixation provided a safe and effective method for the management of vaginal pouch prolapse. Long-term follow-up is planned. To our knowledge, this is the first report describing surgical repair of primary prolapse of a blind vaginal pouch in the setting of MRKH.
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Conflicts of interest
Written informed consent wasobtained from the patient for publication of this video article and any accompanying images.
Written informed consent was obtained from the patient for publication of this video article and any accompanying images.
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Botros, C., Iyer, S., Tran, A.M. et al. Vaginal vault prolapse in a patient with Mayer–Rokitansky–Küster–Hauser syndrome: a video case presentation. Int Urogynecol J 28, 1747–1749 (2017). https://doi.org/10.1007/s00192-017-3325-4
- Mayer–Rokitansky–Küster–Hauser syndrome
- Vaginal vault prolapse