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Vaginal vault prolapse in a patient with Mayer–Rokitansky–Küster–Hauser syndrome: a video case presentation

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Abstract

Introduction and hypothesis

Several reports have described vaginal prolapse in Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome patients after creation of a neovagina. To our knowledge, no reports of primary vaginal prolapse of a blind pouch without previous intervention, or surgery for this condition, have been described.

Methods

In this case report, we describe a 19-year-old woman with MRKH and complete prolapse of her shortened vaginal pouch. Surgical correction utilizing permanent suture-based sacrospinous ligament fixation was performed.

Results

The patient had a successful outcome.

Conclusions

Sacrospinous ligament fixation provided a safe and effective method for the management of vaginal pouch prolapse. Long-term follow-up is planned. To our knowledge, this is the first report describing surgical repair of primary prolapse of a blind vaginal pouch in the setting of MRKH.

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References

  1. 1.

    Londra L, Chuong FS, Kolp L. Mayer-Rokitansky-Kuster-Hauser syndrome: a review. Int J Womens Health. 2015;7:865–70.

  2. 2.

    Morcel K, Lavoué V, Jaffre F, Paniel BJ, Rouzier R. Sexual and functional results after creation of a neovagina in women with Mayer-Rokitansky-Küster-Hauser syndrome: a comparison of nonsurgical and surgical procedures. Eur J Obstet Gynecol Reprod Biol. 2013;169(2):317–20.

  3. 3.

    Kisku S, Varghese L, Kekre A, Sen S, Karl S, Mathai J, et al. Bowel vaginoplasty in children and young women: an institutional experience with 55 patients. Int Urogynecol J. 2015;26(10):1441–8.

  4. 4.

    Kuhn A, Neukomm C, Dreher EF, Imobersteg J, Mueller MD. Prolapse and sexual function 8 years after neovagina according to shears: a study of 43 cases with Mayer-von-Rokitansky-Hauser syndrome. Int Urogynecol J. 2013 Jun;24(6):1047–52.

  5. 5.

    Freundt I, Toolenaar TA, Jeekel H, Drogendijk AC, Huikeshoven FJ. Prolapse of the sigmoid neovagina: report of three cases. Obstet Gynecol. 1994;83(5 Pt 2):876–9.

  6. 6.

    Swenson CW, DeLancey JO, Schimpf MO. Left-sided sacrospinous ligament suspension for treating recurrent sigmoid neovagina prolapse. Int Urogynecol J. 2014;25(11):1593–5.

  7. 7.

    Zhu L, Chen N, Lang J. Vault prolapse of sigmoid neovagina 26 years after vaginoplasty in Mayer-Rokitansky-Kuster_Hauser-syndrome: a case report. Int Urogynecol J. 2013;24(1):179–80.

  8. 8.

    Moriarty CR, Miklos JR, Moore RD. Laparoscopic Davydov correction of a failed gracilis flap neovagina in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome with a pelvic kidney. J Minim Invasive Gynecol. 2013;20(2):262–5.

  9. 9.

    Loveless M, Gutman R, Cundiff G. Tissue expanders optimize harvesting of full-thickness skin grafts in select patients undergoing McIndoe neovagina. J Pelvic Med Surg. 2008;14(3):185–90.

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Author information

Correspondence to Carolyn Botros.

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Written informed consent wasobtained from the patient for publication of this video article and any accompanying images.

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Written informed consent was obtained from the patient for publication of this video article and any accompanying images.

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A rare case of a young woman with vaginal prolapse (MP4 55059 kb)

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A rare case of a young woman with vaginal prolapse (MP4 55059 kb)

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Botros, C., Iyer, S., Tran, A.M. et al. Vaginal vault prolapse in a patient with Mayer–Rokitansky–Küster–Hauser syndrome: a video case presentation. Int Urogynecol J 28, 1747–1749 (2017). https://doi.org/10.1007/s00192-017-3325-4

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Keywords

  • Mayer–Rokitansky–Küster–Hauser syndrome
  • Vaginal vault prolapse