Der Hautarzt

, Volume 60, Issue 5, pp 420–423 | Cite as

Eruptive inflammatorische disseminierte Porokeratose bei einer 71-jährigen Patientin

Kasuistiken

Zusammenfassung

Die eruptive, inflammatorische disseminierte Porokeratose ist eine sehr seltene Erkrankung, die bislang nur in Einzelfallberichten, vorwiegend bei japanischen Patienten beschrieben wurde. Ihr voran geht eine oft über Jahre asymptomatische disseminierte superfizielle Porokeratose, die dann akut mit massivem Pruritus exazerbiert. Histologisch zeigt sich neben der für die Porokeratose typischen kornoiden Lamelle häufig eine eosinophile Spongiose. Wir beschreiben hier den Fall einer 71-jährigen Patientin mit einer klinisch und histologisch gesicherten eruptiven, inflammatorischen disseminierten Porokeratose.

Schlüsselwörter

Porokeratose Mibelli Kornoide Lamelle Eosinophile Spongiose 

Inflammatory stage of disseminated superficial porokeratosis in a 71-year old patient

Abstract

The inflammatory stage of disseminated superficial porokeratosis is a rare disease, which has only been described in case reports, primarily affecting Japanese patients. After having asymptomatic disseminated superficial porokeratosis for years, a typical patient then experiences a sudden exacerbation with distinct pruritus. Histologically, the lesions may show eosinophilic spongiosis in addition to the characteristic cornoid lamella. We describe a 71-year old patient with clinically and histologically diagnosed inflammatory stage of disseminated superficial porokeratosis.

Keywords

Porokeratosis Mibelli Cornoid lamella Eosinophilic spongiosis 

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Copyright information

© Springer Medizin Verlag 2008

Authors and Affiliations

  1. 1.Universitäts-Hautklinik HeidelbergHeidelbergDeutschland

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