Netherlands Heart Journal

, Volume 15, Issue 6, pp 226–228 | Cite as

Primary monophasic mediastinal, cardiac and pericardial synovial sarcoma: a young man in distress

  • C. de ZwaanEmail author
  • L. A. F. M. van Garsse
  • R. L. H. Jansen
  • R. J. van Suylen
case report


A 19-year-old male was admitted because of exertional dyspnoea. The imaging studies revealed epicardial, pericardial and mediastinal masses. The tumours could not be resected through a minor thoracotomy, only biopsies could be taken. Analyses led to the final diagnosis of a monophasic synovial sarcoma. The patient preferred a conservative and palliative approach. Three months later he died at home. Autopsy demonstrated dramatic extension of the tumour masses. We conclude this report with a discussion on primary cardiac tumours. (Neth Heart J 2007;15:226-8.)

distress sarcoma heart 


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Copyright information

© Bohn Stafleu van Loghum 2007

Authors and Affiliations

  • C. de Zwaan
    • 1
    Email author
  • L. A. F. M. van Garsse
  • R. L. H. Jansen
  • R. J. van Suylen
  1. 1.

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