The Indian Journal of Pediatrics

, Volume 65, Issue 1, pp 149–153

Pentalogy of cantrell

  • Ali Osman Katranci
  • A. Semih Görk
  • Riza Rizalar
  • Mithat Günaydin
  • Ender Aritürk
  • Ferit Bernay
  • Naci Gürses
Clinical Brief

Abstract

Omphalocele is often, associated with various abnormalities. In two patients admitted with omphalocele, we additionally found defects both in the pars stenalis of diaphragm and in the diaphragmatic surface of the pericardium, sternal defect and tetralogy of Fallot. These entities form the components of a syndrome, named pentalogy of Cantrell. It is extremely in the spectrum of midline closure defects that display wide variations and its incidence is very low. Existing cardiac defect is the most important factor influencing morbidity and mortality. Herein we report two cases of pentalogy of Cantrell with the review of the syndrome in the light of literature.

Key words

Omphalocele Diaphragm Tetralogy of Fallot 

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Copyright information

© Dr. K C Chaudhuri Foundation 1998

Authors and Affiliations

  • Ali Osman Katranci
    • 1
  • A. Semih Görk
    • 1
  • Riza Rizalar
    • 1
  • Mithat Günaydin
    • 1
  • Ender Aritürk
    • 1
  • Ferit Bernay
    • 1
  • Naci Gürses
    • 1
  1. 1.Departments of Pediatric SurgeryOndokuz Mayis University Faculty of MedicineSamsunTurkey
  2. 2.Ondokuz Mayis Üniversitesi Tip Fakültesi Çocuk Cerrahisi Anabilim Dali 55139SamsunTürkiye

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