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Gastroenterologia Japonica

, Volume 24, Issue 4, pp 410–413 | Cite as

Portal hypertension secondary to intrahepatic arterio-portal shunt in primary amyloidosis: A case report

  • Takumi Aramaki
  • Hideto Terada
  • Hidemasa Okumura
  • Hitoshi Tsutsui
  • Shinsuke Fujita
  • Takashi Tajiri
  • Toru Ohya
  • Hiroyuki Tajima
Case Report

Summary

Portal hypertension is a rare complication in hepatic amyloidosis. We experienced a case of a 40-year-old man with primary amyloidosis and advanced esophageal varices. Angiographic procedures clearly demonstrated portal hypertension secondary to intrahepatic arterio-portal shunting. Hepatic arterial embolization brought about a disappearance of the A-P shunt and portal hypertension, though rebleeding occured. To our knowledge, this is the first case report in which the pathogenesis of portal hypertension in hepatic amyloidosis was elucidated.

Key words

hepatic amyloidosis intrahepatic arterio-portal shunt portal hypertension primary amyloidosis 

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Copyright information

© The Japanese Society of Gastroenterology 1989

Authors and Affiliations

  • Takumi Aramaki
    • 1
  • Hideto Terada
    • 1
  • Hidemasa Okumura
    • 1
  • Hitoshi Tsutsui
    • 1
  • Shinsuke Fujita
    • 1
  • Takashi Tajiri
    • 2
  • Toru Ohya
    • 3
  • Hiroyuki Tajima
    • 3
  1. 1.The First Department of Internal MedicineNippon Medical SchoolTokyoJapan
  2. 2.Department of SurgeryNippon Medical SchoolTokyoJapan
  3. 3.Department of RadiologyNippon Medical SchoolTokyoJapan

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