The Indian Journal of Pediatrics

, Volume 73, Issue 7, pp 623–625 | Cite as

Jervell-Lange Nielsen syndrome in a family with the long QT syndrome (LQTS)

  • R. K. Mondal
  • B. Karmakar
  • P. K. Chandra
  • U. N. Sarkar
Clinical Brief

Abstract

A child with Jervell-Lange Nielsen syndrome is presented from Kolkata. Family study showed that the other family members are suffering from long QT syndrome. The child had frequent syncopal attack and very prolonged QT interval requiring left cardiac sympathetic denervation and beta-blocker therapy as patient could not afford implantable defibrillator and cardiac pacing.

Key words

LQTS QTc interval Jervell and Lange-Nielsen syndrome 

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Copyright information

© Department of Pediatrics All India Institute of Medical Science 2006

Authors and Affiliations

  • R. K. Mondal
    • 2
  • B. Karmakar
    • 2
  • P. K. Chandra
    • 2
  • U. N. Sarkar
    • 1
  1. 1.Department of Pediatrics MedicineIPGMER & SSKM hospitalKolkata
  2. 2.Department of Cardiovascular and Thoracic SurgeryIPGMER & SSKM hospitalKolkata

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