Pediatric Cardiology

, Volume 3, Issue 4, pp 283–286 | Cite as

Absent pulmonary artery

A hint to its embryogenesis
  • Joachim R. Pfefferkorn
  • Hermann Löser
  • Gabriele Pech
  • Robert Toussaint
  • Fritz Hilgenberg
Article

Summary

Cardiac catheterization was performed in nine patients with unilateral absence of a pulmonary artery. Aortography revealed a diverticulum of the innominate artery in five of six patients in whom the aortic arch and absent pulmonary artery were on opposite sides. It is suggested that the diverticulum indicates fetal systemic blood supply to the affected lung through the distal part of the sixth aortic arch, which—consisting of ductal tissue—obliterated after birth, leaving the diverticulum where the ductus joins the innominate artery.

Key words

Absent pulmonary artery Ductus diverticulum Embryology 

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Copyright information

© Springer-Verlag New York Inc 1900

Authors and Affiliations

  • Joachim R. Pfefferkorn
    • 1
  • Hermann Löser
    • 1
  • Gabriele Pech
    • 1
  • Robert Toussaint
    • 1
  • Fritz Hilgenberg
    • 1
  1. 1.Department of Paediatric CardiologyUniversitäts-KinderklinikMünsterGermany

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