Described are two patients whose primary Sjögren's syndrome presented as leucocytoclastic vasculitis of the skin. One patient initially admitted complaints of dryness of the eyes and the mouth after direct questioning, and serologic testing revealed the presence of Ro/SS-A and La/SS-B antibodies. In the other patient the presence of antinuclear antibodies and rheumatoid factors in serum were the only suggestions of the presence of primary Sjögren's syndrome. Primary Sjögren's syndrome should be considered in patients presenting with leucocytoclastic vasculitis.
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Markusse, H.M., Schoonbrood, M., Oudkerk, M. et al. Leucocytoclastic vasculitis as presenting feature of primary Sjögren's syndrome. Clin Rheumatol 13, 269–272 (1994). https://doi.org/10.1007/BF02249025
- Primary Sjögren's Syndrome