Acta Neurochirurgica

, Volume 135, Issue 3–4, pp 126–130 | Cite as

Crowned dens syndrome: a manifestation of hydroxy-apatite rheumatism

  • S. A. Malca
  • P. H. Roche
  • W. Pellet
  • A. Combalbert
Clinical Articles


Crowned dens syndrome is defined as an association of acute cervical pain and calcifications in the peri-odontoid space. The authors report one case of this rare localization of hydroxy-apatite rheumatism and review 12 similar cases in the literature. This disease affects only adult females. Patients present with inflammatory signs, can be treated with non-steroid anti-inflammatory drugs and recover without sequela. Calcium pyrophosphate dihydrate deposition can also lead to this syndrome. Other perioodontoid calcifications and ossifications, usually asymptomatic, appear only as a radiologically crowned dens.


Crowned odontoid hydroxy-apatite rheumatism occipitocervical region odontoid process 


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Copyright information

© Springer-Verlag 1995

Authors and Affiliations

  • S. A. Malca
    • 1
  • P. H. Roche
    • 1
  • W. Pellet
    • 1
  • A. Combalbert
    • 1
  1. 1.Department of NeurosurgeryHôpital Sainte MargueriteMarseilleFrance

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