Gastrointestinal Radiology

, Volume 11, Issue 1, pp 349–350 | Cite as

Ruvalcaba-Myhre-Smith syndrome: A new consideration in the differential diagnosis of intestinal polyposis

  • Michael A. Foster
  • Ray F. Kilcoyne


We present a case of Ruvalcaba-Myhre-Smith syndrome, which, to our knowledge, has not been reported in the radiologic literature. This rare entity is characterized by intestinal polyps, macrocephaly, and hyperpigmented genital macules. The differentiation of this syndrome from other polyposis syndromes is discussed.

Key words

Gastrointestinal tract, polyposis 


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Copyright information

© Springer-Verlag New York Inc 1986

Authors and Affiliations

  • Michael A. Foster
    • 1
  • Ray F. Kilcoyne
    • 1
  1. 1.Department of RadiologyUniversity of Washington School of MedicineSeattleUSA

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