Pediatric Radiology

, Volume 21, Issue 7, pp 508–510 | Cite as

Radio-ulnar synostosis in Williams syndrome

A frequently associated anomaly
  • K. A. Charvat
  • L. Hornstein
  • A. E. Oestreich
Originals

Abstract

Limitation of supination and pronation of the forearm has been occasionally described in individuals with Williams syndrome. It was found in 26% of 23 subjects examined, and was associated with a spectrum of severity of radio-ulnar synostosis on radiography. The occurrence of this functional motor impairment in a substantial subset of persons with Williams syndrome is relevant, because its evaluation is important in habilitation planning.

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Copyright information

© Springer-Verlag 1991

Authors and Affiliations

  • K. A. Charvat
    • 1
    • 2
  • L. Hornstein
    • 1
    • 2
  • A. E. Oestreich
    • 3
  1. 1.Cincinnati Center for Developmental DisordersChildren's Hospital Medical CenterCincinnatiUSA
  2. 2.Department of PediatricsChildren's Hospital Medical CenterCincinnatiUSA
  3. 3.Department of RadiologyChildren's Hospital Medical Center and University of CincinnatiCincinnatiUSA

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