Behavior Genetics

, Volume 1, Issue 1, pp 43–56 | Cite as

Lack of personality pathology in Turner's syndrome: Relation to cytogenetics, hormones and physique

  • John Money
  • Suzanne Mittenthal


Follow-up of 73 patients withTurner's syndrome (XO) seen since 1953 disclosed the presence of a remarkable “inertia of emotional arousal” in the majority. All patients developed a feminine psychosexual identity. Nine of 28 adult patients were married, and two had adopted children. It is not known whether the emotional inertia is a secondary or a direct consequence of the chromosomal abnormality.


D'après des discussions répétées depuis 1953 avec 73 sujets atteintes deSyndrome Turner (XO), une remarquable absence d'excitation émotionnelle fut observée. Toutes ont developpié une orientation psychosexuelle féminine. Neuf parmi les 28 adultes se sont mariées et deux d'entre elles ont adopté des enfants. I1 est impossible de déterminer si cette inertie émotionnelle est un resultat secondaire ou la conséquence directe de l'absence du chromosome.


Die wiederholte Untersuchung von 73Turner Syndrome (XO) Patienten zeigte eine auffällige Abwesentheit auf von emotioneller Aufregbarkeit. Fast alle Patienten hatten eine weibliche psychosexuelle Einstellung. Neun der 28 Erwachsenen waren verheiratet und zwei hatten Kinder adoptiert. Es ist unmöglich fest zu stellen ob die emotionelle Unterreaktität eine sekundäre oder direkte Folge der Chromosomabnormalität ist.


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Copyright information

© Greenwood Periodicals, Inc. 1970

Authors and Affiliations

  • John Money
    • 1
  • Suzanne Mittenthal
    • 1
  1. 1.Department of Psychiatry and Behavioral Sciences and Department of PediatricsThe Johns Hopkins School of Medicine and HospitalBaltimore

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