Pediatric Radiology

, Volume 10, Issue 3, pp 129–132 | Cite as

Atlanto-axial instability in children with Down syndrome

  • S. M. Pueschel
  • F. H. Scola
  • Claire D. Perry
  • J. C. Pezzullo
Originals

Abstract

One hundred fifty-eight patients with Down syndrome underwent roentgenologic examinations of the cervical spine in neutral position, in hyperflexion, and in hyperextension. Fifteen children with Down syndrome were found to have a distance between the joint surfaces of 5 mm and more. The majority of these children were asymptomatic, one child displayed hyperactive deep tendon reflexes and two children were symptomatic and underwent surgery.

Key words

Subluxation C1−C2 Atlanto-axial instability Down syndrome 

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Copyright information

© Springer-Verlag 1981

Authors and Affiliations

  • S. M. Pueschel
    • 1
    • 3
    • 2
  • F. H. Scola
    • 1
    • 3
    • 2
  • Claire D. Perry
    • 1
    • 3
    • 2
  • J. C. Pezzullo
    • 1
    • 3
    • 2
  1. 1.Department of PediatricsChild Development CenterProvidenceUSA
  2. 2.Department of RadiologyRhode Island HospitalProvidenceUSA
  3. 3.Program in MedicineBrown UniversityProvidenceUSA

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