Pediatric Radiology

, Volume 11, Issue 1, pp 42–45 | Cite as

Infantile hepatic hemangioendothelioma with subsequent malignant degeneration

  • S. G. Kirchner
  • R. M. Heller
  • A. G. Kasselberg
  • H. L. Greene
Short Reports


A 4 year old child was seen because of an enlarging epigastric mass and a rapidly falling hematocrit 31/2 years following steroid treatment for multiple hepatic hemangioendotheliomas. Technetium 99 m sulfur colloid liver scan and hepatic angiography confirmed the presence of a large, vascular mass involving the left lobe of the liver. A left hepatic lobectomy was performed and histopathology showed angiosarcoma. As children with hemangioendotheliomas of the liver begin to survive for longer periods of time, surveillance for the possible development of neoplastic disease is recommended.

Key words

Hemangioendothelioma, hepatic Hemangioendothelioma, malignant degeneration Angiosarcoma, hepatic Neoplasm, hepatic 


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Copyright information

© Springer-Verlag 1981

Authors and Affiliations

  • S. G. Kirchner
    • 1
  • R. M. Heller
    • 1
  • A. G. Kasselberg
    • 2
  • H. L. Greene
    • 3
  1. 1.Department of Radiology and Radiological SciencesVanderbilt University Medical CenterNashvilleUSA
  2. 2.Department of PathologyVanderbilt University Medical CenterNashvilleUSA
  3. 3.Department of PediatricsVanderbilt University Medical CenterNashvilleUSA

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