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Documenta Ophthalmologica

, Volume 26, Issue 1, pp 334–348 | Cite as

A propos des relations entre le galactose et le cristallin

  • Jean Nordmann
Article
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Résumé

L'absence d'activité uridyltransférasique ou galactokinasique est pratiquement toujours accompagnée de cataracte. Dans les deux cas l'état général physique et intellectuel peut être satisfaisant.

Dans certaines cataractes congénitales précoces on a pu mettre en évidence une augmentation de l'incorporation dans le galactose-1-phosphate, mais cette observation demande à être confirmée.

Summary

When the enzymes uridyltransferase and galactokinase do not operate, cataracts are practically constant. In both cases the general physical and psychical state may be satisfactory.

In congenital and early postnatal cataracts the incorporation into galactose-1-phosphate seems to be increased; but more experiments on this special point are needed.

Zusammenfassung

Bei fast vollständigem Fehlen der Uridyltransferase - oder Galaktokinase -Aktivität ist die Katarakt praktisch konstant. Beide Zustände sind mit einem zufriedenstellenden Allgemeinzustand vereinbar.

Bei angeborenen und frühkindlichen Staren wurde der Einbau in das Galaktose-1-Phosphat erhöht gefunden. Dieses Ergebnis muß jedoch durch weitere Versuche bestätigt werden.

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Copyright information

© Dr. W. Junk N.V. 1969

Authors and Affiliations

  • Jean Nordmann
    • 1
  1. 1.Clinique Ophtalmologique de l'Université Hôpital CivilFrance

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