Journal of Neurology

, Volume 242, Issue 5, pp 348–350 | Cite as

Severe cerebellar atrophy in the panencephalopathic type of Creutzfeldt-Jakob disease: a case report

  • V. Otto
  • U. Patzold
  • K. Donhuijsen
  • G. F. Walter
Letters to the Editors


Public Health Cerebellar Atrophy Severe Cerebellar Atrophy Panencephalopathic Type 
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  1. 1.
    Berciano J, Diez C, Polo JM, Pascual J, Figols J (1991) CT appearance of panencepahlopathictype of Creutzfeldt-Jakob disease. J Comput Assist Tomogr 15: 332–334PubMedGoogle Scholar
  2. 2.
    Brown P, Cathala F, Castaigne P, Gajdusek DC (1986) Creutzfeld-Jakob disease: clinical analysis of a consecutive series of 230 neuropathologically verified cases. Ann Neurol 20: 597–602PubMedGoogle Scholar
  3. 3.
    Brown P, Gibbs CJ Jr, Rodgers-Johnson P, Asher DM, Sulima MP, Bacote A, Goldfarb LG, Gajdusek DC (1994) Human spongioform encephalopathy: The National Institutes of Health series of 300 cases of experimentally transmitted disease. Ann Neurol 35: 513–529PubMedGoogle Scholar
  4. 4.
    Galvez S, Cartier L (1984) Computed tomography findings in 15 cases of Creutzfeldt-Jakob disease with histological verification. J Neurol Neurosurg Psychiatry 47: 1244–1246PubMedGoogle Scholar
  5. 5.
    Gertz HJ, Henkes H, Cervos-Navarro J (1988) Creutzfeldt-Jakob disease: correlation of MRI and neuropathological findings. Neurology 38: 1481–1482PubMedGoogle Scholar
  6. 6.
    Jellinger K, Heiss WD, Deisenhammer EV (1974) The ataxic (cerebellar) form of Creutzfeldt-Jakob disease. J Neurol 207: 289–305PubMedGoogle Scholar
  7. 7.
    Jones HR Jr, Hedley-Whyte ET, Freidberg SR, Baker RA (1985) Ataxic Creutzfeldt-Jakob disease: diagnostic techniques and neuropathological findings in early disease. Neurology 35: 254–257PubMedGoogle Scholar
  8. 8.
    Kawata A, Suga M, Oda M, Hayashi H, Tanabe H (1992) Creutzfeldt-Jakob disease with congophilic kuru plaques: CT and neuropathological findings of the cerebral white matter. J Neurol Neurosurg Psychiatry 55: 849–851PubMedGoogle Scholar
  9. 9.
    Kitagawa Y, Gotoh F, Koto A, Ebihara S, Okayasu H, Ishii T, Matsuyama H (1983) Creutzfeldt-Jakob disease: a case with extensive white matter degeneration and optic atrophy. J Neurol 229: 97–101PubMedGoogle Scholar
  10. 10.
    Kovanen J, Erkinjuntti T, Iivanainen M, Ketonen L, Haltia M, Sulkava R, Sipponen JT (1985) Cerebral MR and CT imaging in Creutzfeldt-Jakob disease. J Comput Assist Tomogr 9: 125–128PubMedGoogle Scholar
  11. 11.
    Krueger H, Meesmann C, Rohrbach E, Mueller J, Mertens HG (1990) Panencephalopathic type of Creutzfeldt Jakob disease with primary extensive involvement of white matter. Eur Neurol 30: 115–119PubMedGoogle Scholar
  12. 12.
    Mizutani T, Okumura A, Oda M, Shiraki H (1981) Panencephalopathic type of Creutzfeldt-Jakob disease: primary involvement of the cerebral white matter. J Neurol Neurosurg Psychiatry 44: 103–115PubMedGoogle Scholar
  13. 13.
    Roos R, Gajdusek DC, Gibbs CJ Jr (1973) The clinical characteristics of transmissible Creutzfeldt-Jakob disease. Brain 96: 1–20PubMedGoogle Scholar
  14. 14.
    Schlenska GK, Walter GF (1989) Serial computed tomography findings in Creutzfeldt-Jakob disease. Neuroradiology 31: 303–306PubMedGoogle Scholar

Copyright information

© Springer-Verlag 1995

Authors and Affiliations

  • V. Otto
    • 4
  • U. Patzold
    • 1
  • K. Donhuijsen
    • 2
  • G. F. Walter
    • 3
  1. 1.Department of NeurologyStädtisches Klinikum BraunschweigGermany
  2. 2.Department of PathologyStädtisches KlinikumBraunschweigGermany
  3. 3.Department of NeuropathologyMedizinische HochschuleHannoverGermany
  4. 4.Department of NeurologyUniversity of LübeckLübeckGermany

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