Pediatric Nephrology

, Volume 9, Issue 1, pp 36–38

Renal-pancreatic-hepatic dysplasia in siblings

  • Douglas L. Blowey
  • Bradley A. Warady
  • David L. Zwick
  • Catherine Ong
Original Article


Fewer than 20 children with complete renal-pancreatic-hepatic dysplasia have been reported since first described in 1959. We report two brothers with renal-pancreatic-hepatic dysplasia, one of whom had hypertrophic cardiomyopathy and pancreatic exocrine insufficiency, previously unreported associated findings.

Key words

Renal-pancreatic-hepatic dysplasia Cystic kidneys Biliary dysgenesis Pancreatic cysts Hypertrophic cardiomyopathy 


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Copyright information

© IPNA 1995

Authors and Affiliations

  • Douglas L. Blowey
    • 1
  • Bradley A. Warady
    • 1
  • David L. Zwick
    • 2
  • Catherine Ong
    • 3
  1. 1.Division of Nephrology, The Children's Mercy HospitalUniversity of Missouri at Kansas CityKansas CityUSA
  2. 2.Division of Pathology, The Children's Mercy HospitalUniversity of Missouri at Kansas CityKansas CityUSA
  3. 3.Division of Cardiology, The Children's Mercy HospitalUniversity of Missouri at Kansas CityKansas CityUSA

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